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Concomitant Temporomandibular Joint Ankylosis and Maxillomandibular Fusion in a Child with Klippel- Feil Syndrome: A Case Report

  • Deepika Pai1
  • Abhay T Kamath2
  • Pushpa Kini3
  • Manish Bhagania4
  • Saurabh Kumar1,*,

1Department of Pedodontics & Preventive Dentistry, Manipal College of Dental Sciences, MAHE (Manipal Academy of Higher Education), Manipal

2Department of Oral & Maxillofacial surgery, Manipal College of Dental Sciences, MAHE (Manipal Academy of Higher Education), Manipal

3Department of Pediatrics, Manipal College of Dental Sciences, MAHE (Manipal Academy of Higher Education), Manipal

4Henry Goldman School of Dental Medicine, Boston University, Massachusetts

DOI: 10.17796/1053-4625-42.5.11 Vol.42,Issue 5,September 2018 pp.386-390

Published: 01 September 2018

*Corresponding Author(s): Saurabh Kumar E-mail: drsaurabh19@yahoo.co.in

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Abstract

Klippel-Feil syndrome (KFS) is classically characterized by fusion of any of the two of seven cervical vertebrae. It is identified by the presence of a triad of clinical signs including short neck, limitation of head and neck movements and low posterior hairline. Unusual bony malformations leading to facial asymmetry is the most common oral manifestation associated with KFS. Such maxillomandibular fusion can also result in restricted mouth opening in children. It's a challenge to provide complete rehabilitation in such children. This paper presents a report of a type II KFS with both maxillomandibular fusion and temporomandibular joint ankylosis which led to the limited mouth opening in a six-year-old child. Also, the child showed an inadequate development of speech, facial asymmetry and compromised oral health owing to the restricted mouth opening. After thorough investigations, surgery was done which restored limited mouth opening which led to normalizing of speech and oral health.

Keywords

Klippel-Feil Syndrome, Maxillomandibular fusion, Temporomandibular joint ankylosis

Cite and Share

Deepika Pai,Abhay T Kamath,Pushpa Kini,Manish Bhagania,Saurabh Kumar. Concomitant Temporomandibular Joint Ankylosis and Maxillomandibular Fusion in a Child with Klippel- Feil Syndrome: A Case Report. Journal of Clinical Pediatric Dentistry. 2018. 42(5);386-390.

URL:

https://www.jocpd.com/articles/10.17796/1053-4625-42.5.11

References

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