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Dimensional Changes in Dental Arches after Complete Dentures Rehabilitation of a Patient with Hypohidrotic Ectodermal Dysplasia: A Case Report with 18-Year Follow-Up

  • Alix Maria Gregory Sawaya de Castro1
  • Maria Salete Nahás Pires Corrêa2
  • Fernanda Nahás Pires Corrêa3
  • Cristiane de Almeida Baldini Cardoso1
  • Stella Ferreira do Amaral1
  • Michele Baffi Diniz1,*,

1Post-graduate Program in Dentistry, Cruzeiro do Sul University, São Paulo, Brazil

2Department of Pediatric Dentistry, School of Dentistry, São Paulo University, São Paulo, Brazil

3School of Dentistry, São Leopoldo Mandic, Campinas, Brazil

DOI: 10.17796/1053-4625-45.6.9 Vol.45,Issue 6,December 2021 pp.421-427

Published: 01 December 2021

*Corresponding Author(s): Michele Baffi Diniz E-mail: mibdiniz@hotmail.com

Abstract

Background: This case report presents the dimensional changes in dental arches in a patient with hypohidrotic ectodermal dysplasia (HED) after complete denture rehabilitation, with an 18-year follow-up period. Case report: The patient had complete anodontia and was successfully rehabilitated with conventional complete dentures at 3, 4, 5, 7, 9, 12, 16, and 21 years of age. Each successive denture was larger and contained more and larger teeth so as to accommodate for the increase in the size of the developing jaw. A series of diagnostic casts were used to measure the dimensional changes in the arch length and width of the alveolar ridge. Cast analysis revealed that there was an increase in arch length and width in both the maxilla and mandible over time. Cephalometric analysis of craniofacial development was performed at 21 years of age, and suggested protrusion of the maxilla and mandible. Conclusions: The absence of teeth due to HED did not affect the dimensional changes in dental arches after complete denture rehabilitation from childhood to adulthood. The prosthetic treatment improved the patient’s social integration and enabled the development of normal dietary habits, speech, and facial esthetics, which in turn led to improved quality of life.

Keywords

Ectodermal dysplasia; Complete anodontia; Complete dentures; Cast analysis

Cite and Share

Alix Maria Gregory Sawaya de Castro,Maria Salete Nahás Pires Corrêa,Fernanda Nahás Pires Corrêa,Cristiane de Almeida Baldini Cardoso,Stella Ferreira do Amaral,Michele Baffi Diniz. Dimensional Changes in Dental Arches after Complete Dentures Rehabilitation of a Patient with Hypohidrotic Ectodermal Dysplasia: A Case Report with 18-Year Follow-Up. Journal of Clinical Pediatric Dentistry. 2021. 45(6);421-427.

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