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Open AccessOrthodontic Treatment in Conjunction with Twin-bock Treatment
and Growth Hormone Therapy in Silver Russell Syndrome
Orthodontic Treatment in Conjunction with Twin-bock Treatment and Growth Hormone Therapy in Silver Russell Syndrome
1University College of Medicine, Seoul, South Korea
2Department of Pediatrics, Eulji General Hospital, Eulji University College of Medicine, Seoul, South, Korea
3Department of Oral and Maxillofacial Surgery, Kyung Hee University Medical Center, Seoul, South Korea
4School of Dentistry, University of Alabama at Birmingham, Birmingham, AL
5Arizona School of Dentistry & Oral Health, A.T. Still University, Mesa
DOI: 10.17796/1053-4628-41.5.392 Vol.41,Issue 5,September 2017 pp.392-397
Published: 01 September 2017
*Corresponding Author(s): Jae Hyun Park E-mail: JPark@atsu.edu.
Abstract
Silver-Russell syndrome (SRS) is a very rare genetic disorder characterized by intrauterine growth retardation, short stature, and typical craniofacial abnormalities including micrognathia. While growth hormone (GH) therapy in children with SRS significantly improves somatic growth, functional orthopedic treatment can also be effective in adolescents with mandibular deficiency. We report the effects of Phase 1 functional orthopedic treatment of a twin-block appliance in conjunction with GH administration in a 9-year-old boy with GH deficiency and SRS, and the result of the subsequent Phase 2 orthodontic treatment.
Keywords
Silver-Russell syndrome, growth hormone, twin-block appliance
Cite and Share
Su-Jin Ko, Ji Young Seo,Yong-Dae Kwon,Kyounga Cheon,Jae Hyun Park. Orthodontic Treatment in Conjunction with Twin-bock Treatment and Growth Hormone Therapy in Silver Russell Syndrome. Journal of Clinical Pediatric Dentistry. 2017. 41(5);392-397.
References
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