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Van der Woude Syndrome: a report of two cases

  • NM King1,*,
  • CHL Cheong1
  • AME Sanares2

1Paediatric Dentistry and Orthodontics, Faculty of Dentistry, The University of Hong Kong, Prince Philip Dental Hospital, 34 Hospital Road, Hong Kong SAR, China

2Department of Paediatric Dentistry, Westmead Centre for Oral Health, Darcy Road, Westmead 2145, NSW, Australia

DOI: 10.17796/jcpd.28.3.t250869457555q58 Vol.28,Issue 3,July 2004 pp.267-271

Published: 01 July 2004

*Corresponding Author(s): NM King E-mail:


Van der Woude syndrome is a rare autosomal dominant condition with high penetrance and variable

expression. It consists of a cleft lip and/or palate pits on the vermilion of the lower lip, and hypodontia.

Two cases of congenital lip pits with cleft lip and alveolus and an isolated cleft palate are described

to illustrate the variable presentation of the clinical features and the importance of early recognition of

Van der Woude syndrome because of the genetic implications.

Cite and Share

NM King,CHL Cheong,AME Sanares. Van der Woude Syndrome: a report of two cases. Journal of Clinical Pediatric Dentistry. 2004. 28(3);267-271.


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