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Open AccessVan der Woude Syndrome: a report of two cases
Van der Woude Syndrome: a report of two cases
1Paediatric Dentistry and Orthodontics, Faculty of Dentistry, The University of Hong Kong, Prince Philip Dental Hospital, 34 Hospital Road, Hong Kong SAR, China
2Department of Paediatric Dentistry, Westmead Centre for Oral Health, Darcy Road, Westmead 2145, NSW, Australia
DOI: 10.17796/jcpd.28.3.t250869457555q58 Vol.28,Issue 3,July 2004 pp.267-271
Published: 01 July 2004
*Corresponding Author(s): NM King E-mail: kingnm@glink.net.hk
Abstract
Van der Woude syndrome is a rare autosomal dominant condition with high penetrance and variable
expression. It consists of a cleft lip and/or palate pits on the vermilion of the lower lip, and hypodontia.
Two cases of congenital lip pits with cleft lip and alveolus and an isolated cleft palate are described
to illustrate the variable presentation of the clinical features and the importance of early recognition of
Van der Woude syndrome because of the genetic implications.
Cite and Share
NM King,CHL Cheong,AME Sanares. Van der Woude Syndrome: a report of two cases. Journal of Clinical Pediatric Dentistry. 2004. 28(3);267-271.
References
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