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Oral manifestations of juvenile hyaline fibromatosis: a case report

  • Manal I. Al-Malik1
  • Ziad A. Rehbini2
  • Ali A. Eltayeb3

1Consultant Pedodontist, Dental Department, Armed Forces Hospital, Jeddah, Saudi Arabia

2Consultant Oral Surgeon, Dental Department, Armed Forces Hospital, Jeddah, Saudi Arabia

3Consultant Pathologist, Pathology Department, Armed Forces Hospital, Jeddah, Saudi Arabia

DOI: 10.17796/jcpd.29.4.c2047g5688017802 Vol.29,Issue 4,October 2005 pp.347-351

Published: 01 October 2005

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Abstract

Hyaline fibromatosis is a rare autosomal recessive disease of connective tissue, characterised by an accumulation of hyaline in the skin as well as various organs. The clinical features include: multiple cutaneous nodules, joint contractures, osteolytic lesions and gingival hypertrophy. This paper reports the case of an 11-year-old boy, who was referred to our dental clinic complaining of pain in his mouth. On examination, the patient had gross maxillary and mandibular gingival hyperplasia, which caused severe feeding difficulties. He also had severe dental decay, mal-positioned teeth and limited mouth opening. Treatment was done under general anesthesia to remove excess gingival tissue and extract the severely decayed teeth. Histological examination confirmed the diagnosis of juvenile hyaline fibro-matosis. It was concluded that patients with this condition have special dental needs. Early diagnosis of the affected children is important in order to start early preventive dental therapy.

Cite and Share

Manal I. Al-Malik,Ziad A. Rehbini,Ali A. Eltayeb. Oral manifestations of juvenile hyaline fibromatosis: a case report. Journal of Clinical Pediatric Dentistry. 2005. 29(4);347-351.

URL:

https://www.jocpd.com/articles/10.17796/jcpd.29.4.c2047g5688017802

References

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