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Open AccessMultiple developmental dental anomalies and hypermobility type Ehlers-Danlos syndrome
Multiple developmental dental anomalies and hypermobility type Ehlers-Danlos syndrome
1Consultant in Pediatric Dentistry Specialty, Royal Medical Services, King Hussein Medical Center, Royal Medical Services
2Pediatric Dentistry, Prince Rashid Bin Al-Hassan Hospital, Royal Medical Services
DOI: 10.17796/jcpd.30.4.72426m58695tg2h0 Vol.30,Issue 4,July 2006 pp.337-341
Published: 01 July 2006
*Corresponding Author(s): Othman M. Yassin E-mail: fbrihani@yahoo.com
Abstract
Concurrent existence of multiple developmental dental anomalies: hypodontia of permanent mandibular incisors, dentin dysplasia, transmigration, root dilaceration, ectopic eruption and delayed eruption combined with systemic abnormal-ities including joint hyperlaxity and skin hyperextensibility aided in diagnosis of a sporadic case of hypermobility type of Ehlers-Danlos syndrome in a Jordanian Arab male. In dental practice the presence of multiple developmental den-tal anomalies expressing simultaneous defects in different stages of tooth development should raise suspicion of possi-ble of manifestation of an underlying systemic abnormality.
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Othman M. Yassin,Farouk B. Rihani. Multiple developmental dental anomalies and hypermobility type Ehlers-Danlos syndrome. Journal of Clinical Pediatric Dentistry. 2006. 30(4);337-341.
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