Article Data

  • Views 577
  • Dowloads 126

Original Research

Open Access

Klippel-Trénaunay Syndrome Manifesting as Gingival Overgrowth and Teeth Agenesis

  • Hakan Ozdemir1,*,
  • Ismail Marakoglu2
  • Melih Akyol3
  • O Fahrettin Goze4
  • Ulvi Kahraman Gursoy5

1Department of Periodontology, Cumhuriyet University, Sivas, Turkey

2Department of Periodontology, Selcuk University, Konya, Turkey

3Department of Dermatology, Cumhuriyet University, Sivas, Turkey

4Department of Pathology Cumhuriyet University, Sivas, Turkey

5Institute of Dentistry, Helsinki University, Helsinki, Finland

DOI: 10.17796/jcpd.34.4.l41414372l4332m1 Vol.34,Issue 4,July 2010 pp.351-354

Published: 01 July 2010

*Corresponding Author(s): Hakan Ozdemir E-mail: hozdemir@cumhuriyet.edu.tr

Abstract

Objective: Klippel-Trénaunay syndrome (KTS) is characterized by triad of venous varicosity, naevus flammeus,and soft/hard tissue hypertrophy. Manifestations of the syndrome in the head and neck region are rare,but in some cases hemangioma of the lips, tongue, and gums, open bite and cross bite, and early tooth eruption are associated with the disease. Study design: We report a 12-year-old KTS patient with gingival hyperplasia,congenital missing teeth, and increased mucosal vascularization as oral manifestations. Results and conclusion: All manifestations of the KTS were observed on the same side of the head, except bilateral missing teeth. Histological examination showed several vascular enlargements in enlarged gingiva. It is suggested that oral manifestations of the syndrome are generally related to the severity of the disease, but they do not always present in the same pattern.

Keywords

Klippel-Trenaunay syndrome, congenital missing teeth, gingival overgrowth

Cite and Share

Hakan Ozdemir,Ismail Marakoglu,Melih Akyol,O Fahrettin Goze,Ulvi Kahraman Gursoy. Klippel-Trénaunay Syndrome Manifesting as Gingival Overgrowth and Teeth Agenesis. Journal of Clinical Pediatric Dentistry. 2010. 34(4);351-354.

References

1. Auluck A, Suhas S, Pai KM. Klippel-Trenaunay syndrome. Oral Dis, 11: 255–258, 2005.

2. Steiner M, Gould AR, Graves SM, Kuerschner TW. Klippel-Trenaunay-Weber syndrome. Oral Surg Oral Med Oral Pathol, 63: 208–215, 1987.

3. Bathi RJ, Agarwal N, Burde KN. Klippel-Trenaunay syndrome (angio osteohypertrophy syndrome): A report of 3 cases. Oral Surg Oral Med Oral Pathol Oral Radiol Endod, 93: 276–80, 2002.

4. Wiedemann HR, Kunze J. Klippel-Trenaunay syndrome. In: Atlas der Klinishen Syndrome, 4th ed. New York: Schattauer, 1995.

5. Kuhl SRJM, Schulze RKW, Kreft A, d’Hoedt B. Epulis granulomatosa as an oral manifestation of Klippel-Trenaunay syndrome. J Oral Pathol Med, 35: 576–578, 2006.

Abstracted / indexed in

Science Citation Index Expanded (SciSearch) Created as SCI in 1964, Science Citation Index Expanded now indexes over 9,500 of the world’s most impactful journals across 178 scientific disciplines. More than 53 million records and 1.18 billion cited references date back from 1900 to present.

PubMed (MEDLINE) PubMed comprises more than 35 million citations for biomedical literature from MEDLINE, life science journals, and online books. Citations may include links to full text content from PubMed Central and publisher web sites.

Biological Abstracts Easily discover critical journal coverage of the life sciences with Biological Abstracts, produced by the Web of Science Group, with topics ranging from botany to microbiology to pharmacology. Including BIOSIS indexing and MeSH terms, specialized indexing in Biological Abstracts helps you to discover more accurate, context-sensitive results.

Google Scholar Google Scholar is a freely accessible web search engine that indexes the full text or metadata of scholarly literature across an array of publishing formats and disciplines.

JournalSeek Genamics JournalSeek is the largest completely categorized database of freely available journal information available on the internet. The database presently contains 39226 titles. Journal information includes the description (aims and scope), journal abbreviation, journal homepage link, subject category and ISSN.

Current Contents - Clinical Medicine Current Contents - Clinical Medicine provides easy access to complete tables of contents, abstracts, bibliographic information and all other significant items in recently published issues from over 1,000 leading journals in clinical medicine.

BIOSIS Previews BIOSIS Previews is an English-language, bibliographic database service, with abstracts and citation indexing. It is part of Clarivate Analytics Web of Science suite. BIOSIS Previews indexes data from 1926 to the present.

Journal Citation Reports/Science Edition Journal Citation Reports/Science Edition aims to evaluate a journal’s value from multiple perspectives including the journal impact factor, descriptive data about a journal’s open access content as well as contributing authors, and provide readers a transparent and publisher-neutral data & statistics information about the journal.

Scopus: CiteScore 2.0 (2022) Scopus is Elsevier's abstract and citation database launched in 2004. Scopus covers nearly 36,377 titles (22,794 active titles and 13,583 Inactive titles) from approximately 11,678 publishers, of which 34,346 are peer-reviewed journals in top-level subject fields: life sciences, social sciences, physical sciences and health sciences.

Submission Turnaround Time

Conferences

Top