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Rare Association of Klippel Feil Syndrome with Cleft Palate and Congenital Cardiac Deformities: A Case Report

  • Priya Subramaniam1,*,
  • KL Girish Babu1
  • Sony Sugnani1

1Department Of Pedodontics And Preventive Dentistry, The Oxford Dental College, Hospital And Research Centre, Bommanahalli, Hosur Road, Bangalore-560068, Karnataka, India.

DOI: 10.17796/jcpd.35.2.y803m42274301u65 Vol.35,Issue 2,March 2011 pp.213-216

Published: 01 March 2011

*Corresponding Author(s): Priya Subramaniam E-mail: drpriyapedo@yahoo.com

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Abstract

Klippel Feil Syndrome comprises of three characteristic deformities of short neck, a low dorsal hair line and restricted neck mobility. This is a case report of Klippel Feil Syndrome and its rare association with cleft of hard and soft palate, coarctation of aorta, dextrocardia and situs inversus. An interdisciplinary approach towards the management included cardiac surgery, cleft repair and complete oral rehabilitation of the patient. Presently the patient is undergoing speech therapy and is under regular follow up.

Keywords

cleft lip and palate, dextrocardia, interdisciplinary approach

Cite and Share

Priya Subramaniam,KL Girish Babu,Sony Sugnani. Rare Association of Klippel Feil Syndrome with Cleft Palate and Congenital Cardiac Deformities: A Case Report. Journal of Clinical Pediatric Dentistry. 2011. 35(2);213-216.

URL:

https://www.jocpd.com/articles/10.17796/jcpd.35.2.y803m42274301u65

References

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