A Rare Case of Gingival Fibromatosis Associated with Hypertrichosis and a Dysmorphic Face

Several forms of hypertrichosis have been described with and without gingival hyperplasia; some of them are recognized as genetic disorder and associated with syndromes. In all reported cases the most striking differences from other are the craniofacial features. We present a case of a 6-year-old boy with hypertrichosis associated with gingival hyperplasia and a characteristic, coarse face and we consider this case to be a distinctive entity.

congenital hypertrichosis, gingival fibromatosis, children.

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