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Atypical Orofacial Conditions in Noonan Syndrome: A Case Report

  • Leo Toureno1
  • Jae Hyun Park1,*,

1Postgraduate Orthodontic Program, Arizona School of Dentistry & Oral Health, A. T. Still University, Mesa, AZ, USA

DOI: 10.17796/jcpd.36.2.81074271088334h2 Vol.36,Issue 2,March 2012 pp.197-202

Published: 01 March 2012

*Corresponding Author(s): Jae Hyun Park E-mail: JPark@atsu.edu

Abstract

Noonan syndrome (NS) is a relatively common condition characterized by chest deformation, congenital heart disease, short stature and distinctive facial features. Due to its genetic heterogeneity NS patients exhibit a range of clinical signs. Severe gingivitis and supernumerary teeth are rarely seen in connection with NS. In addition, there has not been a report on NS patients with atypical bilateral enlargement of the mental foramens and inferior-alveolar canals. This case report describes a NS patient who has undergone growth hormone (GH) therapy and is presenting with classical and rare NS phenotypes.

Keywords

Noonan syndrome (NS), growth hormone (GH), supernumerary teeth

Cite and Share

Leo Toureno,Jae Hyun Park. Atypical Orofacial Conditions in Noonan Syndrome: A Case Report. Journal of Clinical Pediatric Dentistry. 2012. 36(2);197-202.

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