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Original Research
Open AccessFreeman-Sheldon syndrome: dental and orthodontic implications
Freeman-Sheldon syndrome: dental and orthodontic implications
- T. Roberts1
- L. Stephen1
- T. Naidoo1
- K. Fieggen2
- P. Beighton2
1Faculty of Dentistry, University of the Western Cape
2Division of Human Genetics, Faculty of Health Sciences, University of Cape Town
DOI: 10.17796/jcpd.29.3.8576133xh3576n76 Vol.29,Issue 3,July 2005 pp.267-272
Published: 01 July 2005
Abstract
The manifestations of the Freeman-Sheldon syndrome (FSS) in four members of a South African fam-ily of Xhosa stock have been documented. Orofacial manifestations are a major syndromic compo-nent and warrant early, specialized orthodontic intervention. Our protocol for dental management is outlined and suggestions for holistic oro-dental care are provided.
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T. Roberts,L. Stephen,T. Naidoo,K. Fieggen,P. Beighton. Freeman-Sheldon syndrome: dental and orthodontic implications. Journal of Clinical Pediatric Dentistry. 2005. 29(3);267-272.
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