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Atypical Hallerman-Streif Syndrome: A Case Report

  • Manju Gopakumar1
  • Amitha M Hedge1,*,

1Department of Pedodontics and Preventive Dentistry, A.B. Shetty Memorial Institute of Dental Dental Sciences

DOI: 10.17796/jcpd.30.1.91036513g7u55705 Vol.30,Issue 1,January 2006 pp.73-76

Published: 01 January 2006

*Corresponding Author(s): Amitha M Hedge E-mail: amipedo@yahoo.co.in

Abstract

Hallerman Streif syndrome is a rare congenital disorder characterized by dyscephaly, dental anom-alies, proportionate nazism ,hypotrichosis, cutaneous atrophy limited to the head ,bilateral congenital cataracts and bilateral microphthalmia .Despite the marked craniofacial characteristics and oral find-ings,a relative lack of reports in the dental literature has been noted. In this article, a case of a 8 year old boy with dental problems is described.

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Manju Gopakumar,Amitha M Hedge. Atypical Hallerman-Streif Syndrome: A Case Report. Journal of Clinical Pediatric Dentistry. 2006. 30(1);73-76.

References

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