Title
Author
DOI
Article Type
Special Issue
Volume
Issue
Dental Findings and Treatment in Consanguinity Associated Congenital Chronic Familial Neutropenia
1Department of Periodontology, School of Dentistry, Ege University, Izmir, Turkey
2,Department of Periodontology
3Department of Paediatrics, School of Medicine, Ege University, Izmir, Turkey
DOI: 10.17796/jcpd.31.2.x78245364736262k Vol.31,Issue 2,March 2007 pp.123-126
Published: 01 March 2007
*Corresponding Author(s): Nurcan Buduneli E-mail: nurcan.buduneli@ege.edu.tr
The purpose of this report is to describe dental findings and treatment of an 11-year old male patient and a 5-year old female patient, children of first cousins, suffering from severe benign congenital chronic familial neutropenia. This case report emphazises the importance of differential diagnosis of immunodeficiencies including congenital chronic familial neutropenia in the background of severe periodontal diseases and/or diffuse carious lesions in children.
congenital chronic familial neutropenia, dental treatment, neutrophil defects, immunodeficiency
Nurcan Buduneli,Dilsah Cogulu,Levent Kardesler,Necil Kütükçüler. Dental Findings and Treatment in Consanguinity Associated Congenital Chronic Familial Neutropenia. Journal of Clinical Pediatric Dentistry. 2007. 31(2);123-126.
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