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Original Research

Open Access

Netherton Syndrome: Dental Considerations

  • Hannah Ahn1
  • Richard K. Yoon2,*,

1College of Dental Medicine, Columbia University, New York City, New York

2Pediatric Dentistry Residency Program, Division of Pediatric Dentistry, College of Dental Medicine, Columbia University, New York City, New York

DOI: 10.17796/jcpd.34.1.45180h21p2gu5405 Vol.34,Issue 1,September 2009 pp.77-80

Published: 01 September 2009

*Corresponding Author(s): Richard K. Yoon E-mail: rky1@columbia.edu

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Abstract

Triads of congenital erythroderma and ichthyosis, hair shaft abnormalities, and immune dysregulation have been recognized as Netherton's syndrome (NS). A pediatric patient with NS is presented. Clinical manifestations are described along with a pertinent review of the literature.

Keywords

Netherton, syndrome, case, dental

Cite and Share

Hannah Ahn,Richard K. Yoon. Netherton Syndrome: Dental Considerations. Journal of Clinical Pediatric Dentistry. 2009. 34(1);77-80.

URL:

https://www.jjocpd.com/articles/10.17796/jcpd.34.1.45180h21p2gu5405

References

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5. Fartasch M, Williams ML, Elias PM. Altered Lamellar Body Secretion and Stratum Corneum Membrane Structure in Netherton Syndrome: differentiation from other infantile erythrodermas and pathogenic implications. Arch Dermatol, 135(7): 823–32, 1999.

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