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Original Research

Open Access

Wolf-Hirschhorn Syndrome; Oro-Dental Manifestations and Management

  • Roberts T1
  • Stephen LXG1
  • Fieggen K1
  • Beighton P1,*,

1Faculty of Dentistry, University of the Western Cape, Mitchell’s Plain, Cape Town Special Dental Genetic Clinic, Red Cross Memorial Children’s Hospital, Cape Town

DOI: 10.17796/jcpd.34.2.966jw1w227234756 Vol.34,Issue 2,March 2010 pp.173-176

Published: 01 March 2010

*Corresponding Author(s): Beighton P E-mail: Peter.Beighton@uct.ac.za

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Abstract

The major manifestations of the Wolf-Hirschhorn syndrome are developmental delay, short stature, mental impairment and epilepsy. Clefts of the lip and palate are sometimes present. Dental problems which are overshadowed by the major syndromic manifestations warrant appropriate management.

We have documented an affected South African boy, discussed his dental management and reviewed the oro-dental implications of the disorder.

Keywords

Wolf-Hirschhorn, Syndrome, Cytogenetic,Dental,Genetic, Malformation

Cite and Share

Roberts T,Stephen LXG,Fieggen K,Beighton P. Wolf-Hirschhorn Syndrome; Oro-Dental Manifestations and Management. Journal of Clinical Pediatric Dentistry. 2010. 34(2);173-176.

URL:

https://www.jocpd.com/articles/10.17796/jcpd.34.2.966jw1w227234756

References

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