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Original Research

Open Access

Factor XIII Deficiency: Report of Two Cases

  • Poornima P1
  • Shashibhushan K K1
  • Bharath K P1,*,
  • Subba ReddyV V1

1Department of Pedodontics and Preventive Dentistry, College of Dental Sciences, Davangere, Karnataka, India.

DOI: 10.17796/jcpd.35.1.a377042248788418 Vol.35,Issue 1,September 2010 pp.101-104

Published: 01 September 2010

*Corresponding Author(s): Bharath K P E-mail: dr_bharatkp@yahoo.co.in bha.dentist@gmail.com

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Abstract

Factor XIII deficiency is one of the rare clotting factor deficiencies. Although rare, it is an important disorder because of seriousness of its bleeding manifestations, in particular the incidence of intracranial hemorrhage is higher than any other bleeding disorder. Hence an early diagnosis is extremely important where bleeding manifestations can be prevented by prophylactic factor XIII replacement given at every 4-6 week interval. Case1 presents the management of a factor deficiency associated with a very rare blood group AB+ve, while the case 2 reports the successful surgical management with a replacement therapy.

Keywords

Factor XIII deficiency, Clotting factor deficiency, children, dental management.

Cite and Share

Poornima P,Shashibhushan K K,Bharath K P,Subba ReddyV V. Factor XIII Deficiency: Report of Two Cases. Journal of Clinical Pediatric Dentistry. 2010. 35(1);101-104.

URL:

https://www.jjocpd.com/articles/10.17796/jcpd.35.1.a377042248788418

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