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Original Research

Open Access

Management of Oral Lesions in Lesch-Nyham Syndrome

  • Romero Maroto M1,*,
  • Ruiz Duque C1
  • Vincent G1
  • Garcia Recuero I1
  • Romance A1

1Department of Pediatric Dentistry and Orthodontics, Rey Juan Carlos University, Alcorcón, Madrid, Spain.

DOI: 10.17796/jcpd.38.3.km01520788126247 Vol.38,Issue 3,April 2014 pp.247-249

Published: 01 April 2014

*Corresponding Author(s): Romero Maroto M E-mail: martin.romero@urjc.es

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Abstract

Lesh-Nyhan Syndrome is a hereditary disorder that affects the way in which the body handles the production and breakdown of purines. One of its main characteristic is self-mutilation. We present a new appliance which allows healing to occur.

Keywords

Lesch– Nyhan syndrome , self-harm ,self mutilation, appliance , prevention.

Cite and Share

Romero Maroto M,Ruiz Duque C,Vincent G,Garcia Recuero I,Romance A. Management of Oral Lesions in Lesch-Nyham Syndrome. Journal of Clinical Pediatric Dentistry. 2014. 38(3);247-249.

URL:

https://www.jjocpd.com/articles/10.17796/jcpd.38.3.km01520788126247

References

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